Abstract

Case Report

Autoimmune encephalitis associated with an ovarian teratoma in a 29-year old woman

A Plaikner*, A Jacob, J Rother and C Kohler

Published: 15 May, 2019 | Volume 2 - Issue 1 | Pages: 013-016

NMDA receptor encephalitis is a rare disease first described in 2007. Anti-NMDA receptor encephalitis affects mostly young women as neoplasms, mostly ovarian teratomas, are the underlying cause. The disease is caused by antibodies binding to extracellular epitopes of neuronal cell-surface, which leads to an internalization of NMDA-receptors. The characteristic syndrome of patients with anti-NMDAR as well as its recovery follows a certain pattern. Treatment includes immunotherapy and removal of the immunologic trigger. This case report describes a young woman with anti-NMDA receptor encephalitis caused by an ovarian teratoma. 

Read Full Article HTML DOI: 10.29328/journal.cjog.1001018 Cite this Article Read Full Article PDF

Keywords:

Anti-NMDA receptor encephalitis; Ovarian teratoma

References

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Figures:

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